To help inform the standard of care delivered at accredited care centers, the CF Foundation brings together committees of subject matter experts to write guidelines on topics related to the care of people with cystic fibrosis. Committee members include doctors, nurses, respiratory therapists, dietitians, social workers and people with CF and their families.
A panel of pediatric and adult gastroenterologists created this document to summarize and disseminate the existing medical literature regarding cystic fibrosis-specific gastrointestinal disease.
Enteral tube feedings are an important treatment option in cystic fibrosis when oral intake is not adequate to meet nutritional goals. A multidisciplinary Cystic Fibrosis Foundation panel developed consensus evidence-based guidelines on all aspects of care regarding enteral feeding.
There is no consensus on the best model of care for individuals with CF to manage the non-pulmonary complications that persist after lung transplant. This position paper outlines two models of post-transplant care to accomplish optimal CF care after transplant.
As early cystic fibrosis-related diabetes (CFRD) may be clinically silent, these guidelines highlight the importance of regular screening. Management recommendations focus on insulin therapy and ongoing care by a team with knowledge of CF and diabetes.
Prevention, early recognition, and treatment of cystic fibrosis-related bone disease are imperative to sustain bone health. This guideline provides recommendations regarding screening and treatment to optimize bone health in people with CF.
Involvement of the liver and bile ducts in cystic fibrosis can be clinically silent. These guidelines highlight the role of screening in detection of liver involvement in cystic fibrosis.
These guidelines were created to help care center teams to integrate screening and treating depression and anxiety into comprehensive cystic fibrosis care.
Airway clearance therapies improve the efficacy of the mucociliary escalator and elicit a cough. These guidelines reviewed and compared the various techniques and devices.
These guidelines were developed by consensus based on expert opinion and a medical literature review to provide evidence-based recommendations for chronic medication use for lung health maintenance.