The Cystic Fibrosis Foundation assembled a committee to evaluate research advances and revise guidelines for CF-associated liver disease.
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These guidelines were developed by consensus based on expert opinion and a medical literature review to provide evidence-based recommendations for chronic medication use for lung health maintenance.
Allergic bronchopulmonary aspergillosis is a hypersensitivity lung disease that results from exposure to Aspergillus fumigatus and occurs primarily in people with asthma or with cystic fibrosis. These guidelines were developed via a consensus conference of experts in 2003.
These preschool guidelines provide clinical care guidelines for people with cystic fibrosis between 2 and 5 years. It includes 53 recommendations intended to help make informed decisions in the care of preschool-aged children with CF.
Active cycle of breathing technique (ACBT) combines different breathing techniques that help clear mucus from the lungs in three phases. The first phase helps you relax your airways. The second phase helps you to get air behind mucus and clears mucus. The third phase helps force the mucus out of your lungs.
There are different ways to clear your airways. Most are easy to do. Infants and toddlers will need help from a parent or caregiver. Older kids and adults can choose airway clearance techniques (ACTs) that they can do on their own.
Although cystic fibrosis affects many parts of the body, the focus is often on the lungs because of the disease's effect on breathing.
Autogenic drainage (AD) means “self-drainage” and uses different speeds of breathing to move mucus. To do it, your respiratory therapist can teach you how to control your breaths. You will learn how fast and deeply to breathe to fill certain parts of your lungs with air. AD can take some practice and is usually recommended for people age 8 and older.
Chest physical therapy (CPT or Chest PT) is an airway clearance technique (ACT) to drain the lungs, and may include percussion (clapping), vibration, deep breathing, and huffing or coughing.
Coughing is the most basic airway clearance technique (ACT). It can be an involuntary reflex or it can be controlled as a healthy, natural way for the lungs to get rid of mucus.