Borowitz D, Baker RD, Stallings V. Consensus Report on Nutrition for Pediatric Patients with Cystic Fibrosis. J Pediatr Gastroenterol Nutr. 2002 Sep;35(3):246-259. doi: 10.1097/00005176-200209000-00004.I 

Normal growth is associated with good lung function in children with CF. The CF Foundation gathered a team of experts to determine the best ways to ensure good nutrition for healthy growth. Guidelines on pediatric nutrition include:

• Keeping track of growth by measuring:
  • Height or length, weight, head circumference (in infants)
  • Bone health, stage of puberty
  • Pancreatic insufficiency
• Getting the right amount of:
  • Pancreatic enzymes
  • Formula or breastfeeding (for infants)
  • Necessary calories
  • Vitamins, minerals, fatty acids
  • Salt
• Adding additional calories through:
  • Improving eating habits
  • Supplements
  • Tube feedings

Use of These Guidelines

The CF Foundation intends for this executive summary of its guideline to summarize the published guideline. The published guideline summarizes evidence, and provides reasonable clinical recommendations based on that evidence, to clinicians, patients, and other stakeholders. Care decisions regarding individual patients should be made using a combination of these recommendations, the associated benefit-risk assessment of treatment options from the clinical team, the patient's individual and unique circumstances, as well as the goals and preferences of the patients and families that the team serves, as a part of shared decision-making between the patient and clinician.

The guidelines were published in September 2002, they were reviewed in July 2021 and it was determined that no update is needed at this time.