To ensure that people with CF continue to experience steady gains in length and quality of life, the Foundation helps its accredited care centers provide a standard of CF care with guidelines. We base guidelines on the latest research, medical evidence, and consultation with experts on best practices.

Palliative care guidelines provide recommendations to help reduce physical and emotional symptoms and improve quality of life for people with cystic fibrosis throughout their lives.
To aid clinicians, patients, and families in the best use of modulators, the Cystic Fibrosis Foundation sponsored the creation of guidelines to inform discussions and support decision-making.
Cystic fibrosis is a chronic, lifelong disease, requiring treatment that changes with the needs of the person with CF as he or she ages in order to maintain health. The standard of care for CF from infant to adult care is laid out by the Foundation in its clinical practice guidelines.

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Most newborns in the United States are screened for CF at birth through newborn

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These guidelines were developed by consensus based on expert opinion and a medical literature review to guide the monitoring and care of infants who have an abnormal cystic fibrosis newborn

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These preschool guidelines provide clinical care guidelines for people with cystic fibrosis between 2 and 5 years. It includes 53 recommendations intended to help make informed decisions in the care of preschool-aged children with CF.

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These clinical care guidelines from the Cystic Fibrosis Foundation provide recommendations on how best to care for adults with CF.

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These guidelines were developed by consensus based on expert opinion and a medical literature review to guide the monitoring and care of infants who have an abnormal cystic fibrosis newborn
Diagnosing cystic fibrosis is a multistep process. A complete diagnostic evaluation should include a sweat chloride test, a genetic or carrier test and a clinical evaluation at a CF Foundation-accredited care center.

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To help standardize the diagnosis of both infants with positive newborn
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A well-performed and well-interpreted sweat test is the gold standard for accurately diagnosing cystic fibrosis. These guidelines were developed by consensus based on expert opinion and a review of the medical literature.
People with CF are at greater risk of getting lung infections because thick, sticky mucus builds up in their lungs, allowing germs to thrive and multiply. CF lung infections remain a serious and chronic problem for many living with the disease.

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Updated from 2003, these guidelines on infection prevention and control for cystic fibrosis provide recommendations for people with CF, their families, and health care providers to help reduce the spread of germs in the clinic and hospital setting, as well as in everyday life.

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Allergic bronchopulmonary aspergillosis is a hypersensitivity lung disease that results from exposure to Aspergillus fumigatus and occurs primarily in people with asthma or with cystic fibrosis. These guidelines were developed via a consensus conference of experts in 2003.

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Nontuberculous mycobacteria can cause
Because nutrition is so important to a long and high-quality of life for people with CF, the CF Foundation has created several clinical care guidelines related to nutritional and gastrointestinal (GI) issues.
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These clinical care guidelines from the Cystic Fibrosis Foundation provide recommendations for colorectal

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Enteral tube feedings are an important treatment option in cystic fibrosis when oral intake is not adequate to meet nutritional goals. A multidisciplinary Cystic Fibrosis Foundation panel developed consensus evidence-based guidelines on all aspects of care regarding enteral feeding.

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Normal growth is associated with good

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Nutritional support is a vital component of care for patients with cystic fibrosis. These recommendations cover caloric intake, dosing for pancreatic enzyme replacement therapy, and monitoring growth in childhood and weight status in patients of all ages.

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These guidelines present recommendations on vitamin D
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A panel of pediatric and adult gastroenterologists created this document to summarize and disseminate the existing medical literature regarding cystic fibrosis-specific gastrointestinal disease.
Managing other health conditions related to cystic fibrosis is vital to maintaining the health and quality of life for a person living with the disease. Complications of CF can affect many different organ systems and can be caused directly by the malfunctioning CFTR protein or can be a result of treatments for CF.

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As early cystic fibrosis-related diabetes (CFRD) may be clinically silent, these guidelines highlight the importance of regular screening. Management recommendations focus on insulin therapy and ongoing care by a team with knowledge of CF and diabetes.

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Prevention, early recognition, and treatment of cystic fibrosis-related bone disease are imperative to sustain bone health. This guideline provides recommendations regarding

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Involvement of the liver and

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These guidelines were created to help care center teams to integrate

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This executive summary highlights key content from articles reviewing the pathogenesis, diagnosis, and management of CF endocrine disorders.
Healthy lungs and maintaining lung function is central to the health of people with CF. Below is information on CF clinical care guidelines developed to help people with CF improve and maintain respiratory health.

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These guidelines provide recommendations to the cystic fibrosis community regarding the management of advanced cystic fibrosis lung disease (ACFLD), including reducing practice variability, improving the quality of life and survival of those with ACFLD, and identifying future research directions.

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Airway clearance therapies improve the

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These guidelines were developed by consensus based on expert opinion and a medical literature review to provide evidence-based recommendations for

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The purpose of these guidelines is to provide recommendations to the CF community regarding appropriate identification and timely referral of individuals with advanced CF lung disease to transplant centers.
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Hemoptysis and